Primitive Neuroectodermal Tumor of the Kidney with Inferior Vena Caval Thrombus

Authors

  • Phitsanu Mahawong Division of Urology, Department of Surgery, Faculty of Medicine, Chiang Mai University, Chiang Mai, Thailand
  • Teerapon Amornvesukit Division of Urology, Department of Surgery,Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok, Thailand
  • Suchai Soontrapa Division of Urology, Department of Surgery,Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok, Thailand
  • Sanya Sukpanichnant Department of Pathology, Faculty of Medicine, Siriraj Hospital, Mahidol University, Bangkok, Thailand

Keywords:

Kidney, Inferior vena cava, Primitive neuroectodermal, Thrombus

Abstract

Background: Primitive neuroectodermal tumor (PNET) of the kidney is extremely rare.
Objective: The objective is to report a case of neuroectodermal tumor of kidney, result of the treatment
and review of the literatures.
Case report: We reported a case of young female presented with abdominal mass which computed
tomographic scan showed a large inhomogeneous enhancing solid tumor of right kidney with retrohepatic vena
caval thrombus. Radical nephrectomy with vena caval thrombectomy was performed. Histopathology
demonstrated round tumor cells with rosette formation which immunohistochemistry stained positive for CD99
(MIC-2), the characteristic of this tumor. Despite undergoing adjuvant chemotherapy, the patient developed
local recurrences and multiple distant metastases at only 8 months after operation.
Conclusion: The diagnosis of renal PNETs should be considered in young adult patients who presented
with aggressive renal masses at initial presentations. Immunohistochemistry is of invaluable help for making
a definite diagnosis. This particular type of renal tumor is highly aggressive in nature and has poor prognosis
despite any adjuvant treatments.

References

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Published

2010-03-31

How to Cite

1.
Mahawong P, Amornvesukit T, Soontrapa S, Sukpanichnant S. Primitive Neuroectodermal Tumor of the Kidney with Inferior Vena Caval Thrombus. Thai J Surg [Internet]. 2010 Mar. 31 [cited 2024 Dec. 23];31(1). Available from: https://he02.tci-thaijo.org/index.php/ThaiJSurg/article/view/227850

Issue

Vol. 31 No. 1 (2010): January - March

Section

Case Reports

License

Articles must be contributed solely to The Thai Journal of Surgery and when published become the property of the Royal College of Surgeons of Thailand. The Royal College of Surgeons of Thailand reserves copyright on all published materials and such materials may not be reproduced in any form without the written permission.