Cystic Partially Differentiated Nephroblastoma (CPDN): A Rare Variant of Wilms' Tumor

Authors

  • Supatra Chareekaew Department of Surgery, Queen Sirikit National Institute of Child Health (Children's Hospital), Bangkok, Thailand
  • Watanasak Petlek Department of Surgery, Queen Sirikit National Institute of Child Health (Children's Hospital), Bangkok, Thailand

Abstract

Cystic partially differentiated nephroblastoma (CPDN) is a rare variant of Wilms' tumor (nephroblastoma). It is an unusual neoplasm with a well-differentiated cystic lesion of the kidney. We herein report a case of a 4 month old boy presented with abdominal distension and left flank mass. Abdominal radiograms showed soft tissue haziness in the left side of the abdomen with no calcification. Abdominal ultrasonograms revealed a large multiseptated cystic mass involving most of the left kidney. CT scan of the abdomen showed a 6X7 cm hypodensed mass with well-defined septa of the left kidney. There was no extension of the tumor to the renal capsule and the lymph nodes showed reactive changes. Left nephrectomy was performed. The pathological diagnosis was cystic partially differentiated nephroblastoma (CPDN). Post-operative course was uneventful and the patient has been doing well since.

References

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Published

2007-03-30

How to Cite

1.
Chareekaew S, Petlek W. Cystic Partially Differentiated Nephroblastoma (CPDN): A Rare Variant of Wilms’ Tumor. Thai J Surg [Internet]. 2007 Mar. 30 [cited 2024 Nov. 23];28(1):11-4. Available from: https://he02.tci-thaijo.org/index.php/ThaiJSurg/article/view/241344

Issue

Vol. 28 No. 1 (2007): January - March

Section

Original Articles

License

Articles must be contributed solely to The Thai Journal of Surgery and when published become the property of the Royal College of Surgeons of Thailand. The Royal College of Surgeons of Thailand reserves copyright on all published materials and such materials may not be reproduced in any form without the written permission.