Sturge- Weber Syndrome : A Case with Choroid Plexus Hemangioma

Authors

  • Pradit Chaiyabud Neurosurgery Unit, Department of Surgery, Ratchaburi Hospital, Ratchaburi, Thailand
  • Sirirat Kittiwongsopon Department of Radiology, Ratchaburi Hospital, Ratchaburi, Thailand
  • Puripakorn Pakdirat Department of Pathology, Ratchaburi Hospital, Ratchaburi, Thailand

Abstract

                   Sturge-Weber syndrome (encephalotrigeminal angiomatosis) is an uncommon neurocutaneous disorder. Not many cases of this syndrome have been under the care of neurosurgeons. The syndrome is characterized principally by facial and leptomeningeal angiomas. Hemorrhage from intracranial angiomas in this syndrome is rare. In contrast, epilepsy occurred in nearly every published case. The only known indication for neuro surgical management is to control intractable seizures. This report describes a case of Sturge-Weber syndrome who presented with clinical subarachnoid hemorrhage. The angioma involving the choroid plexus, which was a probable cause of Ieakage, was demonstrated by computed tomography and surgical removal was performed. Histologic examination revealed a hemangioma of the cavernous type. The literature was reviewed.

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Published

2005-06-30

How to Cite

1.
Chaiyabud P, Kittiwongsopon S, Pakdirat P. Sturge- Weber Syndrome : A Case with Choroid Plexus Hemangioma. Thai J Surg [Internet]. 2005 Jun. 30 [cited 2024 Dec. 23];26(2):60-4. Available from: https://he02.tci-thaijo.org/index.php/ThaiJSurg/article/view/242172

Issue

Vol. 26 No. 2 (2005): April - June

Section

Case Reports

License

Articles must be contributed solely to The Thai Journal of Surgery and when published become the property of the Royal College of Surgeons of Thailand. The Royal College of Surgeons of Thailand reserves copyright on all published materials and such materials may not be reproduced in any form without the written permission.