Case Report on a Mitten Hand Contracture in Epidermolysis Bullosa
Keywords:
Epidermolysis bullosa, Hand deformities, Skin transplantationAbstract
Epidermolysis Bullosa is a disorder characterized by skin fragility. Repetitive injury followed by healing can result in severe deformity due to scarring. The available evidence on whether surgery enhances hand function is somewhat inconclusive because there is a shortage of large, well-controlled studies. Nevertheless, the majority of the data suggest that surgery has the potential to enhance hand function. We present a case of Epidermolysis Bullosa in a 6-year-old patient who presented with bilateral mitten hand deformity. Right-hand contracture, pseudosyndactyly release, and defect resurfacing with a full-thickness skin graft (FTSG) were done. The patient had a smooth recovery and regained the ability to grasp objects.
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