Eccrine syringofibroadenoma: A rare case report in a patient with chronic lymphedema

Authors

  • Puangjai Varapornpipat Division of Dermatology, Department Of Medicine, Phramongkutklao Hospital, Bangkok
  • Kobkul Aunhachoke Division of Dermatology, Department Of Medicine, Phramongkutklao Hospital, Bangkok

Keywords:

lymphedema, eccrine syringofibroadenoma

Abstract

Eccrine syringofibroadenoma (ESFA) is an uncommon adnexal tumor of eccrine ductal differentiation with variable clinical presentations and characteristic histopathological features. ESFA usually presents as a solitary, large hyperkeratotic verrucous nodule affecting the extremities. Histopathological findings show anastomosing cords and strands of uniform cuboidal cells embedded in fibrovascular stroma. It can be classified into 5 categories: solitary ESFA, multiple ESFA with hidrotic ectodermal dysplasia, multiple ESFA without associated cutaneous finding, unilateral linear ESFA and reactive ESFA. We report a case of reactive eccrine syringofibroadenoma in a patient with chronic lymphatic obstruction.

References

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Published

2017-06-01

How to Cite

Varapornpipat, P., & Aunhachoke, K. (2017). Eccrine syringofibroadenoma: A rare case report in a patient with chronic lymphedema. Thai Journal of Dermatology, 33(2), 180–185. Retrieved from https://he02.tci-thaijo.org/index.php/TJD/article/view/159249

Issue

Section

Case Report