Familial exudative vitreoretinopathy (FEVR) presenting with vitreous hemorrhage in 60-year-old and 22-year-old Thai women

Authors

  • Taweevat Attaseth Rayong Hospital

Keywords:

Familial exudative vitreoretinopathy, vitreous hemorrhage, adult

Abstract

Abstract

Purpose: To report vitreous hemorrhage as the initial manifestation of adult-onset familial exudative vitreoretinopathy (FEVR)

Methods: Case reports

Results: A 60-year-old and 22-year-old women presented with vitreous hemorrhage in one eye. Fundus examination and wide field fluorescein angiography of both patients showed typical characteristics of FEVR including an increased number of peripheral vessel, straightening of vessels and peripheral avascular retina with neovascularization. Fundus fluorescein angiography-guided laser photocoagulation were performed with good visual outcome in both patients.

Conclusion: Although FEVR is an uncommon cause of vitreous hemorrhage in adult, ophthalmologists should be aware of this condition. Misdiagnosis can lead to serious complications such as retinal detachment and vitreous hemorrhage. Meticulous peripheral retinal examination is needed. Moreover, wide-field fluorescein angiography is essential in diagnosis and management of FEVR.

References

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Published

2021-12-27

Issue

Section

Case Report