Kawasaki disease shock syndrome (KDSS)

Abstract

Kawasaki disease (KD) is an acute febrile vasculitic syndrome of unknown etiology that occurs predominantly in infants and young children. The disease has also been called mucocutaneous lymph node syndrome or infantile periarteritis nodosa. Affected children present with high fever, rash, conjunctival injection, inflammation of the lips or oral cavity, cervical lymphadenitis, erythema and edema of the hands and feet. Cardiac sequelae, the most potentially life-threatening complications include coronary artery aneurysms or ectasia which can occur in up to 15-25% of untreated patients and may lead to myocardial infarction, sudden death, or ischemic heart disease.¹