Arrhythmogenic Right Ventricular Dysplasia (ARVD) Diagnosis In The Elderly
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Published:
Sep 20, 2012
Keywords:
ARVD, arrhtythmia, right ventricular dysplasia
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Abstract
Arrhythmogenic right ventricular dysplasia (ARVD) is a type of nonischemic cardiomyopathy which primarily involves the right ventricle (RV). ARVD is considered a major cause of sudden death in young adults, mainly in the age group under thirty years old and is rarely found in the elderly. Males are predominantly affected.1-3 ARVD has been proposed as a genetic inherited disease with autosomal dominant and various penetrance patterns.4, 5 ARVD is pathologically characterized by fibro-fatty or fatty replacement of the right ventricular myocardial tissue. The fatty form is presented by almost complete replacement without endocardial thinning and found almost exclusively on the RV myocardium. The fibro-fatty replacement is defined as a fatty replacement with endocardial thinning less than 3 mm thickness6.
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How to Cite
1.
Arunakul I- orn, Chaothawee L, Suchato C. Arrhythmogenic Right Ventricular Dysplasia (ARVD) Diagnosis In The Elderly. BKK Med J [Internet]. 2012 Sep. 20 [cited 2024 Nov. 13];4(1):74. Available from: https://he02.tci-thaijo.org/index.php/bkkmedj/article/view/217980
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Case Report
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References
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2. Basso C, Thiene G, Corrado D, et al. Arrhythmogenic right ventricular cardiomyopathy. Dysplasia, dystrophy, or myocarditis?. Circulation 1996;94:983-91.
3. Braunwald E, Libby P, Zipes DD. Heart Disease: A Textbook of Cardiovascular Medicine. 6th ed. WB Saunders 2001: 324-4, 863-89, 2052-6.
4. Ahmad F, Li D, Karibe A , et al. Localization of a gene responsible for arrhythmogenic right ventricular dysplasia to chromosome 3p23. Circulation 1998;98: 2791-5.
5. Rampazzo A, Nava A, Danieli GA, et al. The gene for arrhythmogenic right ventricular cardiomyopathy maps to chromosome 14q23-q24. Hum Mol Genet 1994;3:959-62.
6. Thiene G, Nava A, Corrado D, et al. Right ventricular cardiomyopathy and sudden death in young people N Engl J Med 1988;318:129-133.
7. Basso C, Calabrese F, Corrado D, et al. Postmortemdiagnosis in sudden cardiac death victims: macroscopic ,microscopic and molecular findings . CardiovascularResearch 2001;50:290-300.
8. Fontaine G, Fontaliran F, frank R. Arrhythmogenic rightventricular cardiomyopathies:clinical forms and maindifferential diagnoses (editorial). Circulation 1998;97:1532-5.
9. Richardson P, McKenna W, Bristow M. Report of the1995 World Health Organization/International Societyand Federation of Cardiology Task Force on the Definitionand Classification of cardiomyopathies. Circulation.1996;93:841-2.
10. Gorrado D, Fonteine G, Marcus FI, et al. Arrhythmogenicright ventricular dysplasia cardiomyopathy : needfor an international registry: Circulation 2000; 101:101-6.
11. McKenna WJ, Thiene G, Nava A, et al. Diagnosis ofarrhythmogenic right ventricular dysplasia cardiomyopathy.Br Heart J 1994;71:215-8.
12. Marcus FI, McKenna WJ, Sherrill D, et al. Diagnosisof arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia : Proposed Modification of the Task Criteria.Circulation 2010;121:1533-41.
13. García-Quintana A, Ortega-Trujillo JR, Fernández-Aceytuno AM . Arrhythmogenic Right VentricularDysplasia in the Elderly. Rev Esp Cardiol. 2007;60:87-9
14. Marx, John. Rosen’s emergency medicine: concepts andclinical practice 7th edition. Philadelphia, PA: Mosby/Elsevier 2010:1869.
15. Khurram N, Bomma C, Tandri H, et al. Electrocardiographic features of Arrythmogenic Right VentricularDysplasia/Cardiomyopathy According to Disease Severity:A Need to Broaden Diagnostic .Circulation2004;110:1527-34.
16. Jain R, Dalal D, Daly A, et al. Electrocardiographicfeatures of arrhythmogenic right ventricular dysplasia.Circulation 2009;120:477-87.
17. Khan A, Mittal S, Sherrid MV. et al. ARVD: from geneticto treatment. Anadolu Kardiyol Derg 2009;9:24-31.
18. Burke A, Farb A, Tashko G, et al. Arrhythmogenic RightVentricular cardiomyopathy and fatty replacement of theright ventricular myocardium: are they different disease?Circulation 1998;97:1571-80.
19. Metha D , Davies MJ , Ward DE, et al. Ventricular tachycardia of right ventricular origin: markers of subclinical right ventricular disease. Am Heart J 1994; 127:360-6.
20. Frank I. Marcus, William J. et al. Diagnosis ofArrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia. Proposed Modification of the Task ForceCriteria. Circulations 2010;121:1533-41.
21. Ricci C, Longo R, Pagnan L, et.al. Magnetic resonanceimaging in right ventricular dysplasia. Am J Cardiol1992;70:1589-95.
22. Corrado D, Basso C, Thiene G. Arrhythmogenic rightventricular cardiomyopathy : diagnosis , prognosis , andtreatment. Heart 2000;83:588-95.
23. Tandri H, Saranathan M, Rodrigue Z, et al. Noninvasivedetection of myocardial fibrosis in arrhythmogenic rightventricular cardiomyopathy using delayed enhancementmagnetic resonance imaging : J Am Coll Cardiol 2005;45:98-103.
2. Basso C, Thiene G, Corrado D, et al. Arrhythmogenic right ventricular cardiomyopathy. Dysplasia, dystrophy, or myocarditis?. Circulation 1996;94:983-91.
3. Braunwald E, Libby P, Zipes DD. Heart Disease: A Textbook of Cardiovascular Medicine. 6th ed. WB Saunders 2001: 324-4, 863-89, 2052-6.
4. Ahmad F, Li D, Karibe A , et al. Localization of a gene responsible for arrhythmogenic right ventricular dysplasia to chromosome 3p23. Circulation 1998;98: 2791-5.
5. Rampazzo A, Nava A, Danieli GA, et al. The gene for arrhythmogenic right ventricular cardiomyopathy maps to chromosome 14q23-q24. Hum Mol Genet 1994;3:959-62.
6. Thiene G, Nava A, Corrado D, et al. Right ventricular cardiomyopathy and sudden death in young people N Engl J Med 1988;318:129-133.
7. Basso C, Calabrese F, Corrado D, et al. Postmortemdiagnosis in sudden cardiac death victims: macroscopic ,microscopic and molecular findings . CardiovascularResearch 2001;50:290-300.
8. Fontaine G, Fontaliran F, frank R. Arrhythmogenic rightventricular cardiomyopathies:clinical forms and maindifferential diagnoses (editorial). Circulation 1998;97:1532-5.
9. Richardson P, McKenna W, Bristow M. Report of the1995 World Health Organization/International Societyand Federation of Cardiology Task Force on the Definitionand Classification of cardiomyopathies. Circulation.1996;93:841-2.
10. Gorrado D, Fonteine G, Marcus FI, et al. Arrhythmogenicright ventricular dysplasia cardiomyopathy : needfor an international registry: Circulation 2000; 101:101-6.
11. McKenna WJ, Thiene G, Nava A, et al. Diagnosis ofarrhythmogenic right ventricular dysplasia cardiomyopathy.Br Heart J 1994;71:215-8.
12. Marcus FI, McKenna WJ, Sherrill D, et al. Diagnosisof arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia : Proposed Modification of the Task Criteria.Circulation 2010;121:1533-41.
13. García-Quintana A, Ortega-Trujillo JR, Fernández-Aceytuno AM . Arrhythmogenic Right VentricularDysplasia in the Elderly. Rev Esp Cardiol. 2007;60:87-9
14. Marx, John. Rosen’s emergency medicine: concepts andclinical practice 7th edition. Philadelphia, PA: Mosby/Elsevier 2010:1869.
15. Khurram N, Bomma C, Tandri H, et al. Electrocardiographic features of Arrythmogenic Right VentricularDysplasia/Cardiomyopathy According to Disease Severity:A Need to Broaden Diagnostic .Circulation2004;110:1527-34.
16. Jain R, Dalal D, Daly A, et al. Electrocardiographicfeatures of arrhythmogenic right ventricular dysplasia.Circulation 2009;120:477-87.
17. Khan A, Mittal S, Sherrid MV. et al. ARVD: from geneticto treatment. Anadolu Kardiyol Derg 2009;9:24-31.
18. Burke A, Farb A, Tashko G, et al. Arrhythmogenic RightVentricular cardiomyopathy and fatty replacement of theright ventricular myocardium: are they different disease?Circulation 1998;97:1571-80.
19. Metha D , Davies MJ , Ward DE, et al. Ventricular tachycardia of right ventricular origin: markers of subclinical right ventricular disease. Am Heart J 1994; 127:360-6.
20. Frank I. Marcus, William J. et al. Diagnosis ofArrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia. Proposed Modification of the Task ForceCriteria. Circulations 2010;121:1533-41.
21. Ricci C, Longo R, Pagnan L, et.al. Magnetic resonanceimaging in right ventricular dysplasia. Am J Cardiol1992;70:1589-95.
22. Corrado D, Basso C, Thiene G. Arrhythmogenic rightventricular cardiomyopathy : diagnosis , prognosis , andtreatment. Heart 2000;83:588-95.
23. Tandri H, Saranathan M, Rodrigue Z, et al. Noninvasivedetection of myocardial fibrosis in arrhythmogenic rightventricular cardiomyopathy using delayed enhancementmagnetic resonance imaging : J Am Coll Cardiol 2005;45:98-103.