The Survival of an Old Lady with ALCAPA

Article Sidebar

PDF
Published: Sep 20, 2013
DOI: https://doi.org/10.31524/bkkmedj.2013.09.007
Keywords:
ALCAPA syndrome, Bland-White-Garland syndrome

Main Article Content

Lertlak Chaothawee, MD
Gumpanart Veerakul, MD
Manasawee Indrabhinduwat, MD

Abstract




The coronary artery system is composed of two major systems, the left and right coronary artery system. Both left and right coronary arteries originate from the aortic left and right coronary cusp respectively. The left anterior descending artery (LAD), the main vessel of the left coronary artery system, is considered to be the most important of the coronary artery system. The LAD supplies the left ventricular anterior wall that plays the main role in the left ventricular pumping function. The right coronary artery system is also considered to be the second most important system that mainly supplies the left ventricular inferior wall. The balance of myocardium blood supply demands an adequate coronary artery blood supply from both systems. If the blood supply to some portion of the myocardium is entirely blocked or the energy demand is much higher than the supply, severe myocardium injury or sudden cardiac death may occur. Total blocking of the left main coronary artery (LMA) and proximal LAD vessel is the main cause of death. How does aperson survive with a total absence of arterial blood supply from the left coronary artery system?




Article Details

How to Cite
1.
Chaothawee L, Veerakul G, Indrabhinduwat M. The Survival of an Old Lady with ALCAPA. BKK Med J [Internet]. 2013 Sep. 20 [cited 2024 Nov. 22];6(1):37. Available from: https://he02.tci-thaijo.org/index.php/bkkmedj/article/view/218615
Issue
Vol. 6 (2013): September
Section
Case Report

This is an open access article distributed under the terms of the Creative Commons Attribution Licence, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

References

1. Bland EF. Congenital anomalies of the coronary arteries: report of an unusual case associated with cardiac hyper trophy. AM Heart J 1933;8:787-801.
2. Dodge-Khatami A, Mavroudis C, Backer CL. Anomalous origin of the left coronary artery from the pulmonary artery: collective review from surgical therapy. Ann Thorac Surg 2002;74:946-55.
3. Lin C-P, Chen Y-P, Chen T-H, et al. Anomalous origin of the left main coronary artery from the main pulmonary artery in a young adult. Circulation 2001;104:1575-6.
4. Wesselhoeft H, Fawcett JS, Johnson AL, et al. Anomalous origin of the left coronary artery from the pulmonary trunk: its clinical spectrum, pathology, and pathophysiology, based on a review of 140 cases with seven further cases. Circulation 1968;38:403-5.
5. Tang WC,Chung YC, Sung-How S, et al. Adult type anomalous origin of the left coronary artery from the pulmonary artery. Acta Cardiol Sin 2007;23:115-8.
6. Fontana RS, Edwards JE. Congenital Cardiac Disease: a Review of 357 Case Studies Pathologically. WB Saunders 1962:291.
7. Purut CM, Sabiston DC Jr. Origin of the left coronary artery from the pulmonary artery in older adults. J Thorac Cardiovasc Surg 1991;102:566.