The Survival of an Old Lady with ALCAPA

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Published: Sep 20, 2013
DOI: https://doi.org/10.31524/bkkmedj.2013.09.007
Keywords:
ALCAPA syndrome, Bland-White-Garland syndrome

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Lertlak Chaothawee, MD
Gumpanart Veerakul, MD
Manasawee Indrabhinduwat, MD

Abstract




The coronary artery system is composed of two major systems, the left and right coronary artery system. Both left and right coronary arteries originate from the aortic left and right coronary cusp respectively. The left anterior descending artery (LAD), the main vessel of the left coronary artery system, is considered to be the most important of the coronary artery system. The LAD supplies the left ventricular anterior wall that plays the main role in the left ventricular pumping function. The right coronary artery system is also considered to be the second most important system that mainly supplies the left ventricular inferior wall. The balance of myocardium blood supply demands an adequate coronary artery blood supply from both systems. If the blood supply to some portion of the myocardium is entirely blocked or the energy demand is much higher than the supply, severe myocardium injury or sudden cardiac death may occur. Total blocking of the left main coronary artery (LMA) and proximal LAD vessel is the main cause of death. How does aperson survive with a total absence of arterial blood supply from the left coronary artery system?




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How to Cite
1.
Chaothawee L, Veerakul G, Indrabhinduwat M. The Survival of an Old Lady with ALCAPA. BKK Med J [Internet]. 2013 Sep. 20 [cited 2024 Dec. 23];6(1):37. Available from: https://he02.tci-thaijo.org/index.php/bkkmedj/article/view/218615
Issue
Vol. 6 (2013): September
Section
Case Report

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