Paget's Disease and Apocrine Carcinoma of Vulva

Abstract

Acase of Paget's disease and apocrine carcinoma of vulva in an 82 years old woman was diagnosed and treated surgically. Three years after the operation the patient was alive and well. The role of recognition and long term follow up are emphasized. 

Extramammary Paget's disease is a rare intraepithelial neoplasm. Common sites of occurrence include the vulva, perianal region and perineum. Vulvar Paget's disease usually occurs in women in her 7th decade of life or older. The lession is usually noninvasive which can be cured by local wide excision. The recurrence is common and a regular long term follow up is mandatory.