A case report : Hughes-Stovin Syndrome
Keywords:
Hughes-Stovin syndrome, Behcet’s disease, massive hemop tysis, thrombophlebitis, multiple pulmonary and/or bronchial aneu rysms, computed tomography of the chestAbstract
Hughes-Stovin Syndrome (HSS) is a very rare clinical disorder characterized by thrombophlebitis and multiple pulmonary and/or bronchial aneurysms. The exact etiology and pathogenesis of HSS is unknown; possible causes include infections and angiodysplasia. HSS has also been considered as a variant of Behcet’s disease.
A case report of young male patient, initially presented with cerebral venous sinus thrombosis. Later, he presented with massive hemoptysis. The computed tomography of the chest demonstrated multiple pulmonary aneurysms. Pathogenesis, computed tomography, surgical pathology and treatment of this syndrome are also briefly discussed.
In young men presenting with venous thrombosis as revealed on imaging examination, with platelet count and coagulation tests within normal and hemoptysis the eventuality of HSS is to be considered.
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