Case report : Opercular Syndrome in Pediatrics

Abstract

Blackground : Opercular syndrome is epilepsy syndrome which uncommon. Patient is presented with oropharyngeal dyskinesia accompanied by aphasia. Electroencephalography revealed slow spike-waves during sleep. Treatment with anti-epileptic drugs or epilepsy surgery may improve the outcome.

Materials and methods : A case report of a girl who had status epilepticus at age of 1 year and 6 months and later develops drooling, difficult swallowing and aphasia. Later has been diagnosed as opercular syndrome is improved with anti-epileptic drugs.

Result : A girl who has diagnosed with opercular syndrome due to status epilepticus resulting in brain damage was diagnosed. Electroencephalogram revealed epileptic activities during sleep. Imaging study shown lesion at opercular region. The patient has been treated with anti-epileptic medications including phenytoin, diazepam, corticosteroid, levetiracetam and lamotrigine. Later, the patient shown clinically improvement.

Conclusion : Opercular syndrome is rare disease. A patient with seizure accompanied by drooling, difficult swallowing and aphasia. Electroencephalogram revealed epileptiform discharge during sleep accompanied

by imaging study shown brain lesion at opercular region. This disease should be considered when the clinical syndrome is presented and should be treated promptly to improve the clinical outcome.