A case of Hailey-Hailey disease in late onset presentation

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Published: Mar 31, 2022
Keywords:
Hailey-Hailey disease late onset

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Patcharasiri Bocam
Ms.
Supitchaya Thaiwat

Abstract

            Hailey-Hailey disease is one of the autosomal dominant genodermatoses which is caused by a mutation of the ATP2C1 gene. Patients usually present between the 2nd and 4th decades of life. Clinical presentations consist of blisters on the erythematous base, crusted erosion and vegetative plaques on intertriginous areas or sites of trauma.
            We report a case of a 67-year-old Thai woman with chronic erythematous crusted plaques on bilateral inguinal areas. The clinical and histopathologic findings were compatible with Hailey-Hailey disease. She first experienced the skin lesions at 59 years old which is much later than the usual age of onset of the disease. She was treated with topical steroids, and resolution was observed within 2 weeks.


 

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How to Cite
1.
Bocam P, Thaiwat S. A case of Hailey-Hailey disease in late onset presentation. R. Thai Army Med. J. [internet]. 2022 Mar. 31 [cited 2025 Dec. 22];75(1):71-5. available from: https://he02.tci-thaijo.org/index.php/rtamedj/article/view/255583
Issue
Vol. 75 No. 1 (2022): January-March 2022
Section
รายงานผู้ป่วย (Case Report)
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