Prenatal Diagnosis of Hypoplastic Left Heart Syndrome: a Case Report

Abstract

Prenatal Diagnosis of Hypoplastic Left Heart Syndrome: a Case Report

Waralak               Yamasmit    MD

Dennopporn        Sudjai           MD

Sornpin                 Amarttasn  MD

Department of Obstetrics and Gynecology, BMA Medical College and Vajira Hospital

A 26-year-old Thai pregnant woman, gravida 3, para 2 was prenatally diagnosed for an isolated hypoplastic left heart syndrome (HLHS) at 32 weeks of gestation by ultrasonography. HLHS is a rare congenital heart disease and is the most severe obstructive lesion of the left side of the heart. Fetal karyotype was revealed 46, XY. No otherfetal anomalies were evidenced. She continued pregnancy until term and delivered male baby with birth weight of 2,564 grams and APGAR scores of 8 at both 1 and 5 minutes. Postnatal echocardiography confirmed the HLHS. Cardiac catheterization with PDA stent placement and pulmonary arteries banding were performed. The infant developed septicemia and died on day 10 after birth.

Vajira Med J 2009 ; 53 : 203-209