Multiple Familial Glomangioma: A Case Report

Authors

  • Kusuman Sriphuwong Institute of Dermatology
  • Pimpa Tantanasrigul Institute of Dermatology

DOI:

https://doi.org/10.14456/jdms.2023.33

Keywords:

Glomuvenous malformations, Glomangiomas, Venous malformations

Abstract

Glomuvenous malformations (GVMs), also known as glomangiomas, are benign localized tumors of the skin, that often appear during infancy and childhood. Diagnosis of glomangiomas is based on clinical and histological features. This was a report of a 31-year-old woman who presented with violaceous plaques on the right upper chest since birth. New lesions continued to develop on the other sites including the right shoulder, right arm, right palm and right leg. Her brother had similar lesions on his left thigh. Incisional biopsy showed multiple dilated cavernous-like, thin-walled vascular spaces surrounded by multiple layers of glomus cells and red blood cells in the lumen. Her clinical and histological features were consistent with the diagnosis of multiple familial glomangioma. The treatment was not required for asymptomatic glomangiomas but the larger and extensive glomangiomas could be treated with laser therapy or sclerotherapy. This patient was treated with Nd: YAG (Excel V) for a reduction in glomangioma size.

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Published

15-06-2023

How to Cite

1.
Sriphuwong K, Tantanasrigul P. Multiple Familial Glomangioma: A Case Report. J DMS [Internet]. 2023 Jun. 15 [cited 2024 Dec. 22];48(2):134-7. Available from: https://he02.tci-thaijo.org/index.php/JDMS/article/view/260116

Issue

Section

Case Report