Primary periocular mucinous eccrine carcinoma : a case report

Abstract

Mucinous eccrine carcinoma of the skin is a rare malignant sweat gland neoplasm of the head, neck and trunk. It may be diagnosed as a metastasis tumor or, which is highly unlikely, as a primary focus. The clinical diagnosis of primary mucinous eccrine carcinoma from other common tumors in the eyelid area may be difficult because this tumor does not have a pathognomonic clinical appearance, and is always asymptomatic. It can be presented as a painless, slow growing mass and is usually ignored by the patient. The essential treatment for primary mucinous eccrine carcinoma is complete surgical excision of this lesion. However, a histopathological examination should be performed first, and a systemic work up should be done to rule out the possibility of a primary tumor elsewhere. We report a patient who presented with primary mucinous adenocarcinoma of the eyelid at Institute of Dermatology and highlight their presentation, clinical course and therapeutic approach.