Maffucci' s Syndrome

Report of A Case

บทคัดย่อ

Maffucci’s syndrome is a congenital, non-hereditary mesodermal dysplasia manifested by enchondromatosis and multiple hemangiomas. The syndrome is frequently associated with mesodermal and non-mesodermal tumor. The sarcomatous transformation of enchondroma is 15-20 percent. The over-all incidence of malignant tumor is 23 per cent. A case of Maffucci’s Syndrome with mutiple hemangiopericytomas is presented for the first time in this report. Non-mesodermal tumor component, tubular adenoma of the breast is detected in the same patient.