Dental Management in a Child with Epidermolytic Ichthyosis: A Case Report

Authors

  • Oratai Tantayanon D.D.S., Nakhonpathom Hospital

Keywords:

epidermolytic ichthyosis, early childhood caries, dental management

Abstract

         Ichthyosis is a heterogeneous family of hereditary keratinisation disorders mostly characterized by scaling patterns or hyperkeratosis of the body. Epidermolytic itchthyosis is a rare case in this group  and disorders that present at birth. The teeth are normally developed but in others there may be defect and likely to develop caries. However, there is little evidence regarding the involvement of oral and dental structures in epidermolytic ichthyosis. This article describes a case of 2 years and 10 month-old female of early childhood caries in epidermolytic ichthyosis and the dental management.

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Published

2021-12-27

How to Cite

1.
Tantayanon O. Dental Management in a Child with Epidermolytic Ichthyosis: A Case Report. Reg 4-5 Med J [internet]. 2021 Dec. 27 [cited 2026 Feb. 23];40(4):559-68. available from: https://he02.tci-thaijo.org/index.php/reg45/article/view/255549