Cardiovascular Presentation in Pheochromocytoma: What We Should be Aware

Rizki  Amalia; Ivana Purnama  Dewi; Louisa Fadjri Kusuma  Wardhani; Budi Susetio  Pikir

doi:10.33192/smj.2022.9

Authors

Rizki Amalia Faculty of Medicine, Airlangga University, Surabaya, Indonesia, **Cardiology and Vascular Medicine Department, Dr. Soetomo General Hospital, Surabaya, Indonesia
Ivana Purnama Dewi Faculty of Medicine, Airlangga University, Surabaya, Indonesia, **Cardiology and Vascular Medicine Department, Dr. Soetomo General Hospital, Surabaya, Indonesia, ***Faculty of Medicine, Duta Wacana Christian University, Yogyakarta, Indonesia
Louisa Fadjri Kusuma Wardhani Faculty of Medicine, Airlangga University, Surabaya, Indonesia, **Cardiology and Vascular Medicine Department, Dr. Soetomo General Hospital, Surabaya, Indonesia
Budi Susetio Pikir Faculty of Medicine, Airlangga University, Surabaya, Indonesia, **Cardiology and Vascular Medicine Department, Dr. Soetomo General Hospital, Surabaya, Indonesia

DOI:

https://doi.org/10.33192/smj.2022.9

Keywords:

Pheochromocytoma, cardiovascular manifestations, endocrine heart disease

Abstract

Pheochromocytoma is a catecholamine-producing tumor that although being a rare disease, it poses diagnostic problems because its clinical presentation often mimics certain diseases, including cardiovascular disorders. The effects of excessive catecholamine secretion cause a variety of cardiovascular presentations ranging from hypertension to life-threatening cases such as hypertensive emergency, shock, supraventricular or ventricular arrhythmias, pulmonary edema, and acute coronary syndromes. The principal medical treatment for pheochromocytoma is a blockade of adrenergic receptors. However, surgical or tumor resection often provides complete resolution of abnormal myocardial dysfunction or arrhythmias, so this approach remains the mainstay of treatment that should be performed as soon as the diagnosis of pheochromocytoma is established. As clinicians, we must be aware of the characteristics of the cardiovascular manifestations of pheochromocytoma to make an earlier diagnosis and more appropriate management.

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