A Congenital Glaucoma Associated with Phakomatosis Pigmentovascularis in Infant Case Report

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Sakaorat Petchyim

Abstract

Phakomatosis Pigmentovascularis (PPV) is the rare condition which has been classified in the same spectrum with Sturge-Weber syndrome, Klippel-Trenaunay-Weber syndrome and oculodermal melanocytosis. PPV is the combination of widespread vascular lesions and extensive pigmentary lesions. We report a 2-monthold-infant with PPV type IIa associated with congenital glaucoma. She showed extensive Port-wine stain, extensive Mongolian spots and Café au lait spots along with soft tissue hypertrophy on her right face. She had buphthalmos
on her right eye and the very high intraocular pressure, so she was diagnosed as congenital glaucoma.

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How to Cite
Petchyim, S. (2017). A Congenital Glaucoma Associated with Phakomatosis Pigmentovascularis in Infant Case Report. Siriraj Medical Journal, 69(4), 217–219. Retrieved from https://he02.tci-thaijo.org/index.php/sirirajmedj/article/view/96744
Section
Case Report