Case Report : Anesthesia in Patient with Segawa’s Disease. Buriram Hospital, Thailand.
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Published:
Apr 27, 2018
Keywords:
Segawa’s disease Anesthesia Caesarean section
Main Article Content
Abstract
Segawa’s disease is a rare hereditary disease characterized by progressive dystonia with diurnal fluctuation. Segawa’s disease is highly responsive to Levodopa and according to rare incidence, there were limited literature and knowledge on anesthesiological management of patient with Segawa’s disease.
This study described the experience of anesthesiological management during three operations of a Segawa’s patient. The patient continuously received Levodopa until the day of operation. Total intravenous anesthesia was provided at the first operation for curettage and general anesthesia was provided in last two operations of caesarean section. There were no perioperative and postoperative complication in three anesthetic procedures.
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How to Cite
Chantakul, S., & Yimrattanabowon, P. (2018). Case Report : Anesthesia in Patient with Segawa’s Disease. Buriram Hospital, Thailand. MEDICAL JOURNAL OF SISAKET SURIN BURIRAM HOSPITALS, 30(2), 91–94. retrieved from https://he02.tci-thaijo.org/index.php/MJSSBH/article/view/120346
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Case Report
References
1. Segawa M. Autosomal dominant GTP cyclohydrolase I (AD GCH 1) deficiency (Segawa disease, dystonia 5; DYT 5). Chang Gung Med J 2009;32:1:1-11.
2. PriscuV, Lurie S, Savir I, Rabinerson D, Hagay Z. The Choice of Anesthesia in Segawa's Syndrome. Journal of Clinical Anesthesia 1998;10:2:153-5.
3. Sinha A, Hartsilver EL. Anesthesia for caesarean section in a patient with dopa-responsive dystonia or Segawa's Syndrome. International Journal of Obstetric Anesthesia 2009; 18:1:67-72.
4. Yam CF, Ho ST, Ho YF. A case of a medically correctable pes cavus deformity-Segawa disease. Hong Kong Journal of Orthopaedic Surgery 2001;5:2:129-32.
5. Nutt JG, Fellman JH. Pharmacokinetics of levodopa. Clin Neuropharmacol 1984;7:l:35-49.
6. Senard JM, Verwaerde P, Rascol O, Montastruc JL. Effects of acute levodopa administration on blood pressure and heart variability in never treated parkinsonians. Hypertens Res 1995;18:Suppl 1:5175-7
7. Culley Deborah J, Brooks Meredith R, Crosby Gregory. Neurologic Disease and Anesthesia. In: Cottrell Jame E, Young William L, edited. Cottrell and Young's Neuroanesthesia 5th.ed. Philadelphia : Mosby Elsevier, 2010:390-9.
2. PriscuV, Lurie S, Savir I, Rabinerson D, Hagay Z. The Choice of Anesthesia in Segawa's Syndrome. Journal of Clinical Anesthesia 1998;10:2:153-5.
3. Sinha A, Hartsilver EL. Anesthesia for caesarean section in a patient with dopa-responsive dystonia or Segawa's Syndrome. International Journal of Obstetric Anesthesia 2009; 18:1:67-72.
4. Yam CF, Ho ST, Ho YF. A case of a medically correctable pes cavus deformity-Segawa disease. Hong Kong Journal of Orthopaedic Surgery 2001;5:2:129-32.
5. Nutt JG, Fellman JH. Pharmacokinetics of levodopa. Clin Neuropharmacol 1984;7:l:35-49.
6. Senard JM, Verwaerde P, Rascol O, Montastruc JL. Effects of acute levodopa administration on blood pressure and heart variability in never treated parkinsonians. Hypertens Res 1995;18:Suppl 1:5175-7
7. Culley Deborah J, Brooks Meredith R, Crosby Gregory. Neurologic Disease and Anesthesia. In: Cottrell Jame E, Young William L, edited. Cottrell and Young's Neuroanesthesia 5th.ed. Philadelphia : Mosby Elsevier, 2010:390-9.
